autores Bruna Donida CARMEN REGLA VARGAS Dinara Jaqueline Moura Gilian Batista Balbueno Guerreiro Roberto Giugliani e Thomaz Cruz Tatiane Grazieil Hammerschmidt
palavras-chave DNA damage N-Acetyl-L-Cysteine Niemann-Pick type C disease Niemann-Pick type C1 coenzyme Q10 fibroblasts culture